Congenital bladder and urethral agenesis: case report and management

Agenesis of bladder and urethra is a rare congenital anomaly with very few live cases reported in the literature so far. We reported two female patients (3 and 6 years old) with bladder and urethral agenesis who presented with urinary incontinence. In both of them, Magnetic Resonant Imaging (MRI) revealed a diagnosis of bladder and urethral agenesis with normal ureters draining into the vagina. They underwent creation of a neobladder and conduit; in both cases, neobladder was constructed from the whole caecum and a part of the ascending colon followed by anastomose of ureters into neobladder in a non-refluxing fashion; appendix was used simultaneously as a continent catheterizable conduit. They both attained urinary continence postoperatively.

کلیدواژه ها:

ectopic ureters ، conduit ، neobladder creation ، bladder agenesis